Caso raro de neoplasia mucinosa de baixo grau do apêndice vermiforme
estudo de caso
DOI:
https://doi.org/10.47519/risi.v3i00.16Palavras-chave:
Pseudomixoma peritoneal, Neoplasias apendiculares, Relato de caso, Tratamento cirúrgicoResumo
As neoplasias mucinosas do apêndice vermiforme constituem um grupo raro e heterogêneo de tumores caracterizados pela produção anormal de mucina e comportamento biológico variável. Trata-se de um estudo de caso, de natureza descritiva e retrospectiva, que relata um caso raro de Neoplasia Mucinosa de Baixo Grau do Apêndice Vermiforme, atendido em um serviço de referência em cirurgia geral. O paciente apresentou evolução clínica compatível com quadro abdominal agudo inicialmente inespecífico, que progrediu em um período de 24 horas para dor localizada em fossa ilíaca direita, associada a sinais clínicos sugestivos de patologia cirúrgica. A avaliação clínica e o exame físico, com presença de sinal de Blumberg positivo, foram determinantes para a indicação de abordagem cirúrgica. Os achados reforçam o papel fundamental da análise histopatológica para a confirmação diagnóstica, bem como a relevância dos exames de imagem na avaliação da extensão da doença e no planejamento do tratamento cirúrgico. A escolha da conduta terapêutica individualizada mostrou-se essencial para a evolução clínica favorável do paciente, destacando a necessidade de manejo cuidadoso para prevenir complicações, como a disseminação peritoneal.
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